
{"id":127927,"date":"2025-07-30T12:05:02","date_gmt":"2025-07-30T10:05:02","guid":{"rendered":"https:\/\/ibecbarcelona.eu\/?p=127927"},"modified":"2025-07-30T12:13:12","modified_gmt":"2025-07-30T10:13:12","slug":"fibrosens-project-receives-funds-from-afm-telethon-to-develop-sensor-devices-for-muscular-dystrophy","status":"publish","type":"post","link":"https:\/\/ibecbarcelona.eu\/ca\/el-projecte-fibrosens-rep-financament-de-afm-telethon-per-desenvolupar-sensors-per-a-la-distrofia-muscular","title":{"rendered":"El projecte Fibrosens rep finan\u00e7ament de l&#8217;AFM-Telethon per desenvolupar sensors per a la distr\u00f2fia muscular"},"content":{"rendered":"\n<p><strong>L&#8217;investigador de l&#8217;IBEC Juanma Fern\u00e1ndez ha rebut recentment finan\u00e7ament de l&#8217;AFM-Telethon francesa per dur a terme el projecte &#8220;Monitoratge de processos fibr\u00f2tics en cocultius de m\u00fascul esquel\u00e8tic 3D per a Distr\u00f2fies Musculars utilitzant biosensors plasm\u00f2nics&#8221;. L&#8217;objectiu \u00e9s desenvolupar dispositius amb sensors de multiplexaci\u00f3 molecular per aconseguir la capacitat de detecci\u00f3 en l\u00ednia i en temps real per monitorar els marcadors de fibrosi i avaluar la resposta als medicaments en models de distr\u00f2fia muscular <em>in vitro<\/em>.<\/strong><\/p>\n\n\n\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" width=\"1024\" height=\"683\" data-src=\"https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2025\/07\/0M0A6407_OK_editada_recorte_low-1024x683.jpg\" alt=\"\" class=\"wp-image-127906 lazyload\" data-srcset=\"https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2025\/07\/0M0A6407_OK_editada_recorte_low-1024x683.jpg 1024w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2025\/07\/0M0A6407_OK_editada_recorte_low-300x200.jpg 300w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2025\/07\/0M0A6407_OK_editada_recorte_low-768x512.jpg 768w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2025\/07\/0M0A6407_OK_editada_recorte_low-600x400.jpg 600w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2025\/07\/0M0A6407_OK_editada_recorte_low.jpg 1200w\" data-sizes=\"(max-width: 1024px) 100vw, 1024px\" src=\"data:image\/svg+xml;base64,PHN2ZyB3aWR0aD0iMSIgaGVpZ2h0PSIxIiB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciPjwvc3ZnPg==\" style=\"--smush-placeholder-width: 1024px; --smush-placeholder-aspect-ratio: 1024\/683;\" \/><figcaption class=\"wp-element-caption\">Investigadors de l&#8217;IBEC Chiara Ninfali (esquerra) i Juanma Fern\u00e1ndez (dreta).<\/figcaption><\/figure>\n\n\n\n<p>Juanma Fern\u00e1ndez, investigador s\u00e8nior del grup de <a href=\"https:\/\/ibecbarcelona.eu\/biosensors\/\">Biosensors per a Bioenginyeria<\/a> de l&#8217;Institut de Bioenginyeria de Catalunya (IBEC), liderar\u00e0 el Projecte &#8220;Fibrosens: Monitoratge de processos fibr\u00f2tics en cocultius de m\u00fascul esquel\u00e8tic 3D per a Distr\u00f2fies Musculars utilitzant biosensors plasm\u00f2nics&#8221;, en col\u00b7laboraci\u00f3 amb Val\u00e9rie Allamand del <a href=\"https:\/\/www.institut-myologie.org\/\">Centre de Recerca en Miologia, Universitat de la Sorbona, Inserm, Institut de Miologia de Par\u00eds<\/a>. El projecte rebr\u00e0 finan\u00e7ament de l&#8217;organitzaci\u00f3 francesa AFM-Telethon durant un per\u00edode de dos anys. AFM-Telethon, de les sigles en franc\u00e8s d'&#8221;Associaci\u00f3 Francesa contra les Miopaties &#8211; Marat\u00f3 de Televisi\u00f3&#8221;, \u00e9s un esdeveniment televisat anual de captaci\u00f3 de fons a Fran\u00e7a, originat el 1987, que recapta recursos per a la investigaci\u00f3 cient\u00edfica i per donar suport als pacients i les seves fam\u00edlies, durant un programa que dura prop de 30 hores.<\/p>\n\n\n\n<p>La fibrosi no \u00e9s una malaltia <em>per se<\/em>, sin\u00f3 m\u00e9s aviat el resultat de la desregulaci\u00f3 de la resposta de reparaci\u00f3 tissular a conseq\u00fc\u00e8ncia de diverses lesions tissulars, especialment durant els processos inflamatoris cr\u00f2nics. \u00c9s un segell com\u00fa en els m\u00fasculs esquel\u00e8tics de pacients amb malalties neuromusculars com les distr\u00f2fies musculars de Duchenne i Becker, la distr\u00f2fia muscular cong\u00e8nita d&#8217;Ullrich i les s\u00edndromes de distr\u00f2fia miot\u00f2nica. La limitada informaci\u00f3 que deriva de la investigaci\u00f3 del proc\u00e9s de fibrosi, actualment en models de ratol\u00ed, va motivar la proposta del projecte Fibrosens, que t\u00e9 com a objectiu tancar la bretxa translacional en la comprensi\u00f3 dels processos fibr\u00f2tics en les distr\u00f2fies musculars per aconseguir ter\u00e0pies efectives per als pacients.<\/p>\n\n\n\n<p>El projecte t\u00e9 tres enfocaments principals interconnectats: (1) \u00fas de cocultius 3D de bioenginyeria que imiten el proc\u00e9s de fibrosi que ocorre en els m\u00fasculs dels pacients, (2) identificaci\u00f3 de biomarcadors de fibrosi en el sobrenadant d&#8217;aquests cultius, i (3) desenvolupament de sensors nanoplasm\u00f2nics (dispositius amb sensors \u00f2ptics que exploren les interaccions llum-mat\u00e8ria en estructures met\u00e0l\u00b7liques) per detectar aquests biomarcadors de manera directa i r\u00e0pida. La converg\u00e8ncia de tots aquests enfocaments permetr\u00e0 la fabricaci\u00f3 d&#8217;una plataforma de detecci\u00f3 per monitorar de forma efectiva i en temps real els biomarcadors de fibrosi.<\/p>\n\n\n\n<blockquote class=\"wp-block-quote is-layout-flow wp-block-quote-is-layout-flow\">\n<p><em><em>La tecnologia de detecci\u00f3 nanoplasm\u00f2nica de Fibrosens permetr\u00e0 un cribratge complet de diversos biomarcadors de fibrosi en un sol pas i en pocs minuts. El disseny microflu\u00eddic escalable amb alta sensibilitat i selectivitat minimitzar\u00e0 els falsos positius en el diagn\u00f2stic i seguiment de la malaltia<\/em><\/em>.<\/p>\n\n\n\n<p><em>Juanma Fern\u00e1ndez,<em> investigador s\u00e8nior de l&#8217;IBEC<\/em><\/em><\/p>\n<\/blockquote>\n\n\n\n<p>En resum, Fibrosens desenvolupar\u00e0 una innovadora plataforma de testatge de f\u00e0rmacs que permetr\u00e0 dur a terme proves m\u00e9s r\u00e0pides i econ\u00f2miques de candidats a f\u00e0rmacs antifibr\u00f2tics, reduint aix\u00ed les fases precl\u00edniques. A m\u00e9s, la integraci\u00f3 de c\u00e8l\u00b7lules derivades de pacients amb mutacions espec\u00edfiques o condicions cl\u00edniques en els dispositius permetr\u00e0 realitzar cribratges de f\u00e0rmacs personalitzats, la qual cosa permetr\u00e0 provar quin tractament disponible ser\u00e0 la millor opci\u00f3 espec\u00edficament per a un pacient o un grup de pacients amb una mutaci\u00f3 en particular.<\/p>\n\n\n\n<p>En el futur, aquesta nova tecnologia permetr\u00e0 utilitzar sensors a la cl\u00ednica com a eina de diagn\u00f2stic o monitoritoratge de la fibrosi en pacients. Cal destacar tamb\u00e9 que, at\u00e8s que la fibrosi \u00e9s una caracter\u00edstica comuna en moltes malalties musculars, aquesta plataforma es podria fer servir per a una \u00e0mplia gamma de pacients.<\/p>\n\n\n\n<pre class=\"wp-block-preformatted\">El projecte Fibrosens s'ha concedit per AFM-Telethon amb el n\u00famero 24865 (FERNANDEZ-COSTA Juan M.).<\/pre>\n\n\n\n<figure class=\"wp-block-image size-large is-resized\"><img decoding=\"async\" width=\"1024\" height=\"311\" data-src=\"https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2025\/07\/Fibrosens-logo2-1024x311.jpg\" alt=\"\" class=\"wp-image-127913 lazyload\" style=\"--smush-placeholder-width: 1024px; --smush-placeholder-aspect-ratio: 1024\/311;width:200px\" data-srcset=\"https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2025\/07\/Fibrosens-logo2-1024x311.jpg 1024w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2025\/07\/Fibrosens-logo2-300x91.jpg 300w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2025\/07\/Fibrosens-logo2-768x234.jpg 768w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2025\/07\/Fibrosens-logo2-1536x467.jpg 1536w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2025\/07\/Fibrosens-logo2.jpg 1749w\" data-sizes=\"(max-width: 1024px) 100vw, 1024px\" src=\"data:image\/svg+xml;base64,PHN2ZyB3aWR0aD0iMSIgaGVpZ2h0PSIxIiB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciPjwvc3ZnPg==\" \/><\/figure>\n\n\n\n<p><\/p>\n","protected":false},"excerpt":{"rendered":"<p>L&#8217;investigador de l&#8217;IBEC Juanma Fern\u00e1ndez ha rebut recentment finan\u00e7ament de l&#8217;AFM-Telethon francesa per dur a terme el projecte &#8220;Monitoratge de processos fibr\u00f2tics en cocultius de m\u00fascul esquel\u00e8tic 3D per a Distr\u00f2fies Musculars utilitzant biosensors plasm\u00f2nics&#8221;. L&#8217;objectiu \u00e9s desenvolupar dispositius amb sensors de multiplexaci\u00f3 molecular per aconseguir la capacitat de detecci\u00f3 en l\u00ednia i en temps real per monitorar els marcadors de fibrosi i avaluar la resposta als medicaments en models de distr\u00f2fia muscular in vitro.<\/p>\n","protected":false},"author":37,"featured_media":127907,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[98],"tags":[2140,1999,1131,1852],"post_formats":[],"class_list":["post-127927","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-noticies-institucionals","tag-biosensor-ca","tag-biosensors-for-bioengineering-ca","tag-javier-ramon-ca","tag-malalties-neuromusculars"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.3 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>El projecte Fibrosens rep finan\u00e7ament de l&#039;AFM-Telethon per desenvolupar sensors per a la distr\u00f2fia muscular - Institute for Bioengineering of Catalonia<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/ibecbarcelona.eu\/ca\/el-projecte-fibrosens-rep-financament-de-afm-telethon-per-desenvolupar-sensors-per-a-la-distrofia-muscular\/\" \/>\n<meta property=\"og:locale\" content=\"ca_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"El projecte Fibrosens rep finan\u00e7ament de l&#039;AFM-Telethon per desenvolupar sensors per a la distr\u00f2fia muscular - Institute for Bioengineering of Catalonia\" \/>\n<meta property=\"og:description\" content=\"L&#039;investigador de l&#039;IBEC Juanma Fern\u00e1ndez ha rebut recentment finan\u00e7ament de l&#039;AFM-Telethon francesa per dur a terme el projecte &quot;Monitoratge de processos fibr\u00f2tics en cocultius de m\u00fascul esquel\u00e8tic 3D per a Distr\u00f2fies Musculars utilitzant biosensors plasm\u00f2nics&quot;. L&#039;objectiu \u00e9s desenvolupar dispositius amb sensors de multiplexaci\u00f3 molecular per aconseguir la capacitat de detecci\u00f3 en l\u00ednia i en temps real per monitorar els marcadors de fibrosi i avaluar la resposta als medicaments en models de distr\u00f2fia muscular in vitro.\" \/>\n<meta property=\"og:url\" content=\"https:\/\/ibecbarcelona.eu\/ca\/el-projecte-fibrosens-rep-financament-de-afm-telethon-per-desenvolupar-sensors-per-a-la-distrofia-muscular\/\" \/>\n<meta property=\"og:site_name\" content=\"Institute for Bioengineering of Catalonia\" \/>\n<meta property=\"article:published_time\" content=\"2025-07-30T10:05:02+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2025-07-30T10:13:12+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2025\/07\/0M0A6407_OK_editada_recorte_low.jpg\" \/>\n\t<meta property=\"og:image:width\" content=\"1200\" \/>\n\t<meta property=\"og:image:height\" content=\"800\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"author\" content=\"Sarah Moreira\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Escrit per\" \/>\n\t<meta name=\"twitter:data1\" content=\"Sarah Moreira\" \/>\n\t<meta name=\"twitter:label2\" content=\"Temps estimat de lectura\" \/>\n\t<meta name=\"twitter:data2\" content=\"4 minuts\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\\\/\\\/schema.org\",\"@graph\":[{\"@type\":\"Article\",\"@id\":\"https:\\\/\\\/ibecbarcelona.eu\\\/ca\\\/el-projecte-fibrosens-rep-financament-de-afm-telethon-per-desenvolupar-sensors-per-a-la-distrofia-muscular\\\/#article\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/ibecbarcelona.eu\\\/ca\\\/el-projecte-fibrosens-rep-financament-de-afm-telethon-per-desenvolupar-sensors-per-a-la-distrofia-muscular\\\/\"},\"author\":{\"name\":\"Sarah Moreira\",\"@id\":\"https:\\\/\\\/ibecbarcelona.eu\\\/#\\\/schema\\\/person\\\/d3a158b8d448000777023ca1e3d71d34\"},\"headline\":\"El projecte Fibrosens rep finan\u00e7ament de l&#8217;AFM-Telethon per desenvolupar sensors per a la distr\u00f2fia muscular\",\"datePublished\":\"2025-07-30T10:05:02+00:00\",\"dateModified\":\"2025-07-30T10:13:12+00:00\",\"mainEntityOfPage\":{\"@id\":\"https:\\\/\\\/ibecbarcelona.eu\\\/ca\\\/el-projecte-fibrosens-rep-financament-de-afm-telethon-per-desenvolupar-sensors-per-a-la-distrofia-muscular\\\/\"},\"wordCount\":693,\"publisher\":{\"@id\":\"https:\\\/\\\/ibecbarcelona.eu\\\/#organization\"},\"image\":{\"@id\":\"https:\\\/\\\/ibecbarcelona.eu\\\/ca\\\/el-projecte-fibrosens-rep-financament-de-afm-telethon-per-desenvolupar-sensors-per-a-la-distrofia-muscular\\\/#primaryimage\"},\"thumbnailUrl\":\"https:\\\/\\\/ibecbarcelona.eu\\\/wp-content\\\/uploads\\\/2025\\\/07\\\/0M0A6407_OK_editada_recorte_low.jpg\",\"keywords\":[\"biosensor\",\"Biosensors for bioengineering\",\"Javier Ram\u00f3n\",\"Malalties neuromusculars\"],\"articleSection\":[\"Not\u00edcies institucionals\"],\"inLanguage\":\"ca\"},{\"@type\":\"WebPage\",\"@id\":\"https:\\\/\\\/ibecbarcelona.eu\\\/ca\\\/el-projecte-fibrosens-rep-financament-de-afm-telethon-per-desenvolupar-sensors-per-a-la-distrofia-muscular\\\/\",\"url\":\"https:\\\/\\\/ibecbarcelona.eu\\\/ca\\\/el-projecte-fibrosens-rep-financament-de-afm-telethon-per-desenvolupar-sensors-per-a-la-distrofia-muscular\\\/\",\"name\":\"El projecte Fibrosens rep finan\u00e7ament de l'AFM-Telethon per desenvolupar sensors per a la distr\u00f2fia muscular - 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