
{"id":55918,"date":"2017-10-30T09:26:04","date_gmt":"2017-10-30T08:26:04","guid":{"rendered":"http:\/\/ibecbarcelona.eu\/?p=55918"},"modified":"2017-10-31T12:52:28","modified_gmt":"2017-10-31T11:52:28","slug":"un-projecte-de-libec-rep-financament-de-la-fundacio-lluita-contra-la-ceguesa","status":"publish","type":"post","link":"https:\/\/ibecbarcelona.eu\/ca\/un-projecte-de-libec-rep-financament-de-la-fundacio-lluita-contra-la-ceguesa\/","title":{"rendered":"Un projecte de l&#8217;IBEC rep finan\u00e7ament de la Fundaci\u00f3 Lluita Contra la Ceguesa"},"content":{"rendered":"<h6 class=\"caption\" style=\"float: left; width: 50%; padding: 0px 30px 10px 0px;\">Esquerra: El Pau amb el Germ\u00e1n L\u00f3pez Fuentes, el president de FARPE-FUNDALUCE.<\/h6>\n<p>&#8220;La tecnologia optogen\u00e8tica permet controlar amb llum l&#8217;activitat neuronal, per\u00f2 requereix de manipulacions gen\u00e8tiques en les c\u00e8l\u00b7lules diana. La fotofarmacologia per la seva banda ofereix resultats equivalents utilitzant f\u00e0rmacs regulats amb llum&#8221;, explica Pau. &#8220;L&#8217;estrat\u00e8gia del nostre projecte consisteix a reempla\u00e7ar els fotorreceptors degenerats amb interruptors moleculars prot\u00e8sics, aplicant-ho en teixits de l&#8217;ull naturalment sensibles a la llum.<\/p>\n<p>El projecte, un &#8216;tour de force&#8217; qu\u00edmic, es basa en un m\u00e8tode per sintetitzar compostos que contenen amines i que poden unir-se covalentment amb la prote\u00efna diana de la retina sense haver de fer manipulacions gen\u00e8tiques. &#8220;Si podem demostrar in vivo la capacitat de recuperaci\u00f3 de la visi\u00f3 d&#8217;aquestes petites mol\u00e8cules, el seu impacte traslacional ser\u00e0 molt alt i les proves cl\u00edniques podrien comen\u00e7ar immediatament&#8221;, diu el Pau.<\/p>\n<p>En el marc de la Federaci\u00f3 d&#8217;Associacions de Retinosis Pigmentaria d&#8217;Espanya (<a href=\"http:\/\/www.retinosisfarpe.org\/index.php\" target=\"_blank\" rel=\"noopener\">FARPE<\/a>), la Fundaci\u00f3 Lluita Contra la Ceguesa (<a href=\"http:\/\/www.retinosisfarpe.org\/quienes-somos\/fundaluce.html\" target=\"_blank\" rel=\"noopener\">FUNDALUCE<\/a>) mant\u00e9 i gestiona un Fons Nacional de Recerca per a la promoci\u00f3 de la recerca cient\u00edfica i m\u00e8dica en la prevenci\u00f3, tractament i cura de les distr\u00f2fies heredit\u00e0ries de retina, principalment la Retinosi Pigment\u00e0ria, que provoca una p\u00e8rdua progressiva de visi\u00f3 en la qual el pacient pateix ceguesa nocturna, reducci\u00f3 de la visi\u00f3 perif\u00e8rica, p\u00e8rdua de l&#8217;agudesa visual, visi\u00f3 de centelleigs que dificulten la visi\u00f3, o canvis en la percepci\u00f3 dels colors. L&#8217;avaluaci\u00f3 dels 8 projectes que es van presentar a la convocat\u00f2ria FUNDALUCE 2016 va ser realitzada per l&#8217;Ag\u00e8ncia Nacional d&#8217;Avaluaci\u00f3 i Prospectiva (ANEP) del MINECO i per un Comit\u00e8 Assessor d&#8217;Experts (CAU) de FARPE i FUNDALUCE.<\/p>\n<p><img decoding=\"async\" class=\"right wp-image-55851 lazyload\" data-src=\"https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2017\/10\/molecular_prosthesesWEB-1.jpg\" alt=\"\" width=\"400\" height=\"216\" data-srcset=\"https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2017\/10\/molecular_prosthesesWEB-1.jpg 500w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2017\/10\/molecular_prosthesesWEB-1-300x162.jpg 300w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2017\/10\/molecular_prosthesesWEB-1-230x124.jpg 230w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2017\/10\/molecular_prosthesesWEB-1-150x81.jpg 150w\" data-sizes=\"(max-width: 400px) 100vw, 400px\" src=\"data:image\/svg+xml;base64,PHN2ZyB3aWR0aD0iMSIgaGVpZ2h0PSIxIiB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciPjwvc3ZnPg==\" style=\"--smush-placeholder-width: 400px; --smush-placeholder-aspect-ratio: 400\/216;\" \/><\/p>\n<h6 class=\"caption\" style=\"float: left; width: 44%; padding: 0px 40px 20px 0px;\">Imatge: estructures neuronals a diferents escales, des de circuits neuronals (esquerra) fins a espines dendr\u00edtiques (centre), tenyides per diverses t\u00e8cniques per microsc\u00f2pia \u00f2ptica i de fluoresc\u00e8ncia. Les pr\u00f2tesis moleculars s\u00f3n compostos sint\u00e8tics (les estructures grises en la imatge de la dreta) que s&#8217;uneixen permanentment a les prote\u00efnes (verda) per proporcionar una determinada funci\u00f3, com la sensibilitat a la llum en una retina degenerada. El compost gris actua com una droga regulada per la llum que activa la prote\u00efna quan s&#8217;il\u00b7lumina.<\/h6>\n<p>La FARPE va ser creada en 1990 per un grup de persones afectades per la Retinosi Pigment\u00e0ria. A Espanya la pateixen al voltant de vint mil persones entre els 2.000.000 de persones afectades per una Distr\u00f2fia Heredit\u00e0ria de Retina. Des de 1998 FUNDALUCE ha donat el seu suport al projecte de recerca cient\u00edfica m\u00e9s rellevant de l&#8217;any que abordi aquesta patologia o altres similars.<\/p>\n<p>Pau es va presentar amb el Projecte d&#8217;excel\u00b7l\u00e8ncia en la  XIX Jornada dels Premis a la Recerca FARPE-FUNDALUCE, que va tenir lloc el 27 d&#8217;octubre a l&#8217;Auditori ONCE de Catalunya, c\/Gran Via dels Corts Catalans 400, Barcelona.<\/p>\n<p>&#8212;<\/p>\n<p><strong>IBEC als mitjans:<\/strong> <a href=\"http:\/\/ecodiario.eleconomista.es\/sociedad\/noticias\/8701697\/10\/17\/Las-xix-jornadas-de-investigacion-sobre-la-retinosis-abordaran-la-lucha-contra-la-ceguera-hereditaria-y-genetica.html\" target=\"_blank\" rel=\"noopener\">http:\/\/ecodiario.eleconomista.es\/sociedad\/noticias\/8701697\/10\/17\/las-xix-jornadas-de-investigacion-sobre-la-retinosis-abordaran-la-lucha-contra-la-ceguera-hereditaria-y-genetica.html<\/a><\/p>\n","protected":false},"excerpt":{"rendered":"<h3><img decoding=\"async\" class=\"left size-full wp-image-55904 lazyload\" data-src=\"https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2017\/10\/pau_german.jpg\" alt=\"\" width=\"450\" height=\"462\" data-srcset=\"https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2017\/10\/pau_german.jpg 450w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2017\/10\/pau_german-292x300.jpg 292w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2017\/10\/pau_german-127x130.jpg 127w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2017\/10\/pau_german-146x150.jpg 146w, https:\/\/ibecbarcelona.eu\/wp-content\/uploads\/2017\/10\/pau_german-45x45.jpg 45w\" data-sizes=\"(max-width: 450px) 100vw, 450px\" src=\"data:image\/svg+xml;base64,PHN2ZyB3aWR0aD0iMSIgaGVpZ2h0PSIxIiB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciPjwvc3ZnPg==\" style=\"--smush-placeholder-width: 450px; --smush-placeholder-aspect-ratio: 450\/462;\" \/>L&#8217;investigador principal de l&#8217;IBEC i professor de recerca ICREA Pau Gorostiza ha guanyat l&#8217;ajuda a la recerca &#8216;FUNDALUCE 2016&#8217;, que consisteix a desenvolupar interruptors moleculars prot\u00e8sics que podrien reempla\u00e7ar als fotorreceptors degenerats en la retina amb l&#8217;objectiu de restaurar la visi\u00f3.<\/h3>\n<p>El projecte \u201cFotoconmutadors covalents per al control remot de receptors end\u00f2gens\u201d, que es dur\u00e0 a terme amb col\u00b7laboradors de l&#8217;IQAC-CSIC, la Universitat Miguel Hern\u00e1ndez, la Universitat d&#8217;Alcal\u00e0 d&#8217;Henares i l&#8217;Institut de Neuroci\u00e8ncies d&#8217;Alacant, proposa el concepte de nanopr\u00f2tesi: si una caracter\u00edstica funcional d&#8217;un \u00f2rgan o teixit est\u00e0 regulada per un receptor, hauria de ser possible utilitzar fotoconmutadors covalents dirigits per controlar aquest receptor particular amb llum, manipulant d&#8217;aquesta manera la seva funci\u00f3.<\/p>\n","protected":false},"author":4,"featured_media":55904,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[98],"tags":[],"post_formats":[],"class_list":["post-55918","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-noticies-institucionals"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.4 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Un projecte de l&#039;IBEC rep finan\u00e7ament de la Fundaci\u00f3 Lluita Contra la Ceguesa - Institute for Bioengineering of Catalonia<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/ibecbarcelona.eu\/ca\/un-projecte-de-libec-rep-financament-de-la-fundacio-lluita-contra-la-ceguesa\/\" \/>\n<meta property=\"og:locale\" content=\"ca_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Un projecte de l&#039;IBEC rep finan\u00e7ament de la Fundaci\u00f3 Lluita Contra la Ceguesa - Institute for Bioengineering of Catalonia\" \/>\n<meta property=\"og:description\" content=\"L&#039;investigador principal de l&#039;IBEC i professor de recerca ICREA Pau Gorostiza ha guanyat l&#039;ajuda a la recerca &#039;FUNDALUCE 2016&#039;, que consisteix a desenvolupar interruptors moleculars prot\u00e8sics que podrien reempla\u00e7ar als fotorreceptors degenerats en la retina amb l&#039;objectiu de restaurar la visi\u00f3.  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